Moira B. Hilscher1, Jonathan N. Johnson2,3, Frank Cetta2,3, David J. Driscoll2,3, John J. Poterucha1, William Sanchez1, Heidi M. Connolly3, Patrick S. Kamath1
Congenital Heart Disease, Vol.12, No.2, pp. 124-132, 2017, DOI:10.1111/chd.12446
Abstract The physiological consequences of the Fontan circulation impose risk for hepatic dysfunction and
may culminate in hepatic fibrosis, cirrhosis, and hepatocellular carcinoma. Consensus regarding
appropriate surveillance modalities to diagnose liver disease in Fontan patients is lacking, in part
due to the relative lack of strong evidence and prospective studies in this patient population. The
goal of this paper is to critically review the current evidence and provide recommendations for the
surveillance of hepatic complications in the post-Fontan patient population. More >