Melissa S.W. Yamauchi1,2, Michael D. Puchalski1,2, Hsin Ti Weng1, Nelangi M. Pinto1,2, Susan P. Etheridge1,2, Angela P. Presson1, Lloyd Y. Tani1,2, L. LuAnn Minich1,2, Richard V. Williams1,2
Congenital Heart Disease, Vol.13, No.3, pp. 432-439, 2018, DOI:10.1111/chd.12591
Abstract Background: Disease progression of an isolated bicuspid aortic valve (BAV) in children is poorly
understood and adult management guidelines may not be applicable. Thus, we sought to evaluate
disease progression of pediatric isolated BAV and its relationship to current management
practices.
Methods: Children with a BAV and ≤mild aortic stenosis (AS) and/or aortic regurgitation (AR)
at the time of initial evaluation were included in this retrospective cohort study (1/2005-12/
2014). Outcomes included change in z-scores for aortic root and ascending aorta diameters,
cardiac interventions, adverse outcomes, recommended follow-up interval, and frequency of
cardiac imaging studies at each… More >