Open Access
EDITORIAL
Shi-Joon Yoo1,2,*, Ankavipar Saprungruang2, Christopher Z. Lam1, Robert H. Anderson3
Congenital Heart Disease, Vol.17, No.5, pp. 495-504, 2022, DOI:10.32604/chd.2022.021155
Abstract In the last issue, two case reports separately present examples of the extremely rare and complex congenital heart diseases that show concordant atrioventricular connections to the L-looped ventricles in the presence of situs solitus. Both cases highlight that the relationship between the two ventricles within the ventricular mass is not always harmonious with the given atrioventricular connection. Such disharmony between the connections and relationships requires careful assessment of the three basic facets of cardiac building blocks, namely their morphology, the relationship of their component parts, and their connections with the adjacent segments. 3D imaging and printing can now facilitate an… More >
Graphic Abstract
Open Access
ARTICLE
Alyssia Venna1, Kathleen Reid2, Sarah Davis2, Jiaxiang Gai3, Yves d’Udekem1, Sarah Clauss2,*
Congenital Heart Disease, Vol.17, No.5, pp. 505-518, 2022, DOI:10.32604/chd.2022.021571
Abstract Background: Patients with single ventricle anatomy are at increased risk of growth failure and malnutrition.
Amongst cardiac centers, there is little standardization of feeding practices in this complex population. We
hypothesized that initiation of our center’s preoperative feeding protocol would result in decreased gastrostomy
tube (G-tube) use, decreased length of stay and would not result in increased Necrotizing Enterocolitis (NEC)
rates. Methods: A single institution review of 52 patients who had undergone stage I single ventricle palliative
repair was performed. Patient diagnoses were hypoplastic left heart syndrome (39%), atrioventricular canal
(15%), and other (46%). Postoperative parameters such as time to… More >
Graphic Abstract
Open Access
ARTICLE
Jodi L. Feinberg1, Peter Sheng2, Stephanie Pena2, Adam J. Small1, Susanna Wendelboe1, Katlyn Nemani3, Vikram Agrawal4, Dan G. Halpern1,*
Congenital Heart Disease, Vol.17, No.5, pp. 519-531, 2022, DOI:10.32604/chd.2022.024174
Abstract Background: Adults with congenital heart disease (ACHD) have increased prevalence of mood and anxiety disorders. There are limited data regarding the influence of the COVID-19 pandemic on the mental health and health behaviors of these patients. Objective: The purpose is to evaluate the perceptions, emotions, and health behaviors of ACHD patients during the COVID-19 pandemic. Methods: In this cross-sectional study of ACHD patients, we administered surveys evaluating self-reported emotions, perceptions and health behaviors. Logistic regressions were performed to determine the adjusted odds of displaying each perception, emotion and health behavior based on predictor variables. Results: Ninety-seven patients (mean age 38.3… More >
Graphic Abstract
Open Access
ARTICLE
Qi Liu, Shoujun Li, Zhongdong Hua*
Congenital Heart Disease, Vol.17, No.5, pp. 533-539, 2022, DOI:10.32604/chd.2022.020496
Abstract Background: Double aortic arch (DAA) with distal left-sided aortic arch atresia (LAAA) can form complete vascular ring by ligamentum connection. We aimed to introduce an uncommon DAA-LAAA diagnosis and treatment by the minimally invasive surgical technique (MIST). Methods: We retrospectively reviewed 7 cases of
DAA-LAAA that were treated from January 2017 to July 2021. All infant patients underwent surgical repair
by minimally invasive surgical technique. Mean follow-up was 14.43 months (range, 5–21 months). Results:
There were seven patients with DAA-LAAA, including six males and one female. Median age was 19.29 months
(range, 9.0–29.0 months). Median weight was 11.30 kg (range,… More >
Graphic Abstract
Open Access
CASE REPORT
Yifan Li1, Zewen Chen2, Jian Zhuang2, Zhiwei Zhang1,*
Congenital Heart Disease, Vol.17, No.5, pp. 541-549, 2022, DOI:10.32604/chd.2022.024907
(This article belongs to this Special Issue: Nightmare Case Reports in Congenital Heart Disease)
Abstract A congenital coronary artery fistula (CCAF) combined with giant coronary aneurysm (CAA) is a rare congenital
cardiac abnormality. We reported an 8-year-old patient who underwent transcatheter closure of both inlet and
outlet of a proximal left coronary artery (LCA)-to-left ventricular (LV) fistula with CAA of 41 mm × 28 mm
in diameter, during which acute occlusion of left anterior descending coronary artery (LAD) occurred immediately after device implantation at the inlet of fistula. We managed to prevent the patient from major adverse cardiac events by conservative therapy with dual antiplatelet agents instead of surgical removal of the device. The
patient… More >
Graphic Abstract
Open Access
CASE REPORT
Elio Caruso1,*, Silvia Farruggio1, Alfredo Di Pino1, Paolo Guccione1, Mohammadrafie Khorgami2
Congenital Heart Disease, Vol.17, No.5, pp. 551-556, 2022, DOI:10.32604/chd.2022.023711
(This article belongs to this Special Issue: Nightmare Case Reports in Congenital Heart Disease)
Abstract We present the case of an infant admitted to our department for a rapid broad complex tachycardia and cardiovascular collapse. The patient was submitted to genetic testing because of a conduction defect at baseline ECG
and family history of gene mutation. A new SCN5A gene mutation variant was found leading to diagnosis of
sodium-channel dysfunction arrhythmia. More >
Graphic Abstract
Open Access
META-ANALYSIS
Ying Yang1,#, Tingting Lv2,#, Siyuan Li1, Ping Zhang1,2,*
Congenital Heart Disease, Vol.17, No.5, pp. 557-567, 2022, DOI:10.32604/CHD.2021.017292
Abstract Background: T-wave alternans (TWA) is a risk factor of ventricular arrhythmias or sudden cardiac death (SCD)
in patients with ischemic cardiomyopathy. Nevertheless, the relationship between TWA and adverse cardiac
events (ACE) in patients with congenital long QT syndrome (LQT) remains controversial. Methods: A systematic
electronic search of PubMed, Embase and the Cochrane Library was conducted from database inception dates to
28 April 2021 and assessed the relationship between TWA and ACE in patients with LQTS. Sub-group analysis
evaluated the association between microvolt TWA (MTWA) and ACE in different monitoring models and ECGlead numbers. Results: A pooled analysis of seven studies… More >
Open Access
ARTICLE
Jae Hee Seol1,4,#, Se Yong Jung1,#, Jae Young Choi1, Han Ki Park2, Young Hwan Park2, Nam Kyun Kim1,3,*
Congenital Heart Disease, Vol.17, No.5, pp. 569-578, 2022, DOI:10.32604/chd.2022.018436
Abstract Objective: Junctional ectopic tachycardia is common after cardiac surgery for congenital heart disease. However,
its incidence and related risk factors in infants after cardiac surgery are not well known. The objective of this study
was to determine the overall incidence and related risk factors for junctional ectopic tachycardia in neonates and
infants. Methods: We enrolled a total of 271 patients aged <1 year who underwent open cardiac surgery at Severance Cardiovascular Hospital from January 2018 to December 2020. Exclusion criteria were immediate postoperative mortality, other arrhythmias detected in the perioperative period, and prematurity. Result: The overall
incidence of junctional ectopic… More >
Open Access
ARTICLE
Eleni P. Asimacopoulos*, Steven J. Staffa, Peter C. Laussen, Kirsten C. Odegard
Congenital Heart Disease, Vol.17, No.5, pp. 579-590, 2022, DOI:10.32604/chd.2022.020334
Abstract Background: Thromboembolic events are a cause of significant morbidity and mortality in the Fontan population. We previously reported on coagulation profile changes in a cohort of patients with hypoplastic left heart
syndrome (HLHS) from Stage I through Fontan completion. In this report, we examine their clinical status, anticoagulation and incidence of thromboembolic events up to 20 years post Fontan. Methods: A retrospective chart
review was conducted for twenty (20) surviving patients, from 1998 through December 2020. Patients who underwent orthotopic heart transplantation (OTx) were followed until their transplant. Patients who were found in the
original study to have a factor… More >
Open Access
ARTICLE
Benjamin Zielonka1,2,*, David M. Harrild1,2, Sunil J. Ghelani1,2, Eleni G. Elia1,2, Christopher W. Baird3,4, Andrew J. Powell1,2, Rahul H. Rathod1,2
Congenital Heart Disease, Vol.17, No.5, pp. 591-603, 2022, DOI:10.32604/chd.2022.021509
Abstract Background: The right ventricle to pulmonary artery conduit (RVPAC) may impair right ventricular (RV) function in patients with functional single right ventricles. Modification of the RVPAC using a ring-reinforced end
with dunked insertion into the RV through a limited ventriculotomy may reduce the impact on RV function.
We compared RV segmental strain between patients with a traditional RVPAC and ring-reinforced RVPAC using
feature tracking cardiovascular magnetic resonance (CMR) imaging. Methods: Patients with CMR examinations
after Stage I operation with RVPAC between 2000 and 2018 were reviewed. Ventricular mass, volumes, late gadolinium enhancement (LGE), and peak radial and circumferential strain of… More >