Open Access

CASE REPORT

Concordant Atrioventricular Connection to L-Looped Ventricles with the Left Ventricle on Top of the Right Ventricle in Situs Solitus: A Case Report with 3D Modelling and Printing

Mi Kyoung Song¹, Gi Beom Kim¹, Woong Han Kim², Whal Lee³, Eun-Jung Bae^1,*

1 Department of Pediatrics, Seoul National University Children’s Hospital, Seoul National University College of Medicine, Seoul, Korea
2 Department of Thoracic and Cardiovascular Surgery, Seoul National University Children’s Hospital, Seoul, Korea
3 Department of Radiology and the Institute of Radiation Medicine, Seoul National University Hospital, Seoul, Korea

* Corresponding Author: Eun-Jung Bae. Email:

Congenital Heart Disease 2022, 17(4), 393-398. https://doi.org/10.32604/chd.2022.019603

Received 06 February 2022; Accepted 08 June 2022; Issue published 04 July 2022

Abstract

We report the case of a rare complex cardiac anomaly involving situs solitus, concordant atrioventricular connection with left-hand ventricular topology, and L-looped ventricles. The ventricles had a superior-inferior relationship with an inferiorly located right ventricle, which had a double outlet with far posteriorly located great arteries. The left atrium was elongated, with juxta-positioned atrial appendages on the right side. The 3D-printed model using a computed tomography scan taken on the fourth day of birth demonstrated the anatomy clearly and helped us decide on the surgical management.

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Graphic Abstract

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