@Article{CHD.2021.015749, AUTHOR = {Hao Hong, Nianguo Dong, Mingxing Xie, Lin Li, Si Chen, Wengang Sun, Xiaoqing Hu}, TITLE = {A Rare Long Term Survival Case of Complete Pentalogy of Cantrell in Adult after One-Staged Surgery}, JOURNAL = {Congenital Heart Disease}, VOLUME = {16}, YEAR = {2021}, NUMBER = {5}, PAGES = {513--518}, URL = {http://www.techscience.com/chd/v16n5/42687}, ISSN = {1747-0803}, ABSTRACT = {Pentalogy of Cantrell is a rare congenital abnormality. Even with high-quality medical care and staged corrective surgeries in professional hospitals, the mortality rate is still very high and long-term prognosis is poor. Survival is largely determined by the complexity and severity of cardiac abnormalities, the efficiency of abdominal wall closure and postoperative complications. A 24-year-old male patient with complete pentalogy of Cantrell was diagnosed. One-stage surgical repair of all abnormalities were completed. The patient recovered well and had been follow-up for 7 years. He has a good cosmetic outcome, with no signs of cardiac dysfunction. No complications were noted.}, DOI = {10.32604/CHD.2021.015749} }