Open Access

CASE REPORT

A Rare Long Term Survival Case of Complete Pentalogy of Cantrell in Adult after One-Staged Surgery

Hao Hong¹, Nianguo Dong^1,*, Mingxing Xie², Lin Li², Si Chen¹, Wengang Sun³, Xiaoqing Hu²
1 Department of Cardiovarscular Surgery, Union Hospital, Tongji Medical College, Huazhong University of Science and Technology, Wuhan, 430022, China
2 Department of Ultrasound, Union Hospital, Tongji Medical College, Huazhong University of Science and Technology, Wuhan, 430022, China
3 Department of Radiology, Union Hospital, Tongji Medical College, Huazhong University of Science and Technology, Wuhan, 430022, China
* Corresponding Author: Nianguo Dong. Email:

Congenital Heart Disease 2021, 16(5), 513-518. https://doi.org/10.32604/CHD.2021.015749

Received 10 January 2021; Accepted 08 April 2021; Issue published 03 June 2021

Abstract

Pentalogy of Cantrell is a rare congenital abnormality. Even with high-quality medical care and staged corrective surgeries in professional hospitals, the mortality rate is still very high and long-term prognosis is poor. Survival is largely determined by the complexity and severity of cardiac abnormalities, the efficiency of abdominal wall closure and postoperative complications. A 24-year-old male patient with complete pentalogy of Cantrell was diagnosed. One-stage surgical repair of all abnormalities were completed. The patient recovered well and had been follow-up for 7 years. He has a good cosmetic outcome, with no signs of cardiac dysfunction. No complications were noted.

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Keywords

Pentalogy of cantrell; adult; one-stage surgery

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