Open Access

CASE REPORT

Scimitar Syndrome: Role of Right Atrial Longitudinal Strain. A Case Report

Isabella Leo¹, Jolanda Sabatino^1,2,3, Sabrina La Bella¹, Antonio Strangio¹, Iolanda Aquila¹, Concetta Procopio¹, Carmen Anna Maria Spaccarotella¹, Maria Petullà⁴, Salvatore De Rosa^1,2, Ciro Indolfi^1,2,5,*
1 Division of Cardiology, Department of Medical and Surgical Sciences, Magna Graecia University, Catanzaro, Italy
2 Cardiovascular Research Center, Magna Graecia University, Catanzaro, Italy
3 Department of Paediatric Cardiology, Royal Brompton Hospital, London, UK
4 Department of Radiology, Magna Graecia University, Catanzaro, Italy
5 Mediterranea Cardiocentro, Napoli, Italy
* Corresponding Author: Ciro Indolfi. Email:

Congenital Heart Disease 2021, 16(4), 411-416. https://doi.org/10.32604/CHD.2021.015062

Received 09 November 2020; Accepted 22 January 2021; Issue published 19 April 2021

Abstract

We describe a case of a rare congenital heart disorder, scimitar syndrome, diagnosed in an adult woman presenting with dyspnea on exertion, chest pain and recurrent episodes of pulmonary infections. The hallmark of the syndrome is the presence of an enlarged anomalous pulmonary vein draining into the inferior vena cava. Speckle tracking echocardiography, including the often-forgotten atrial strain evaluation, is a sensitive parameter that should be routinely used for a better clinical and prognostic evaluation of patients with congenital heart disease (CHD).

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Keywords

Scimitar syndrome; RV overload; congenital heart disease; myocardial strain

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