Open Access

ARTICLE

Kathrine Rydén Suther^1,*, Charlotte de Lange^1,2, Henrik Brun³, Rolf Svendsmark¹, Bac Nguyen¹, Stig Larsen⁴, Bjarne Smevik¹, Arnt Eltvedt Fiane^5,6, Harald Lauritz Lindberg⁶, Einar Hopp¹
Congenital Heart Disease, Vol.16, No.2, pp. 107-121, 2021, DOI:10.32604/CHD.2021.014164
Abstract Background: Patency of the coronary arteries is an issue after reports of sudden cardiac death in patients with transposition of the great arteries (TGA) operated with arterial switch (ASO). Recent studies give rise to concern regarding the use of ionising radiation in congenital heart disease, and assessment of the coronary arteries with coronary MR angiography (CMRA) might be an attractive non-invasive, non-ionising imaging alternative in these patients. Theoretically, the use of 3.0T CMRA should improve the visualisation of the coronary arteries. The objective of this study was to assess feasibility of 3.0T CMRA at the coronary artery origins by comparing… More >

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ARTICLE

Misook Seo¹, In-Kyung Song², Hye-Mee Kwon², Byungdoo Andrew Lee², Won-Jung Shin^2,*
Congenital Heart Disease, Vol.16, No.2, pp. 123-136, 2021, DOI:10.32604/CHD.2021.012626
Abstract Background: In patients with cyanotic congenital heart disease (CHD), cerebral oxygenation may be maintained by elevations in hematocrit (Hct). Hemodilution accompanying cardiopulmonary bypass (CPB), however, can disrupt cerebral oxygen balance, leading to fluctuations in cerebral oxygen saturation (ScO₂). The present study investigated the effects of Hct changes on the fluctuation of ScO₂ during CPB in cyanotic CHD using performance measurement (PM). Methods: Children with CHD (51 acyanotic and 46 cyanotic) who had undergone cardiac surgery using CPB were enrolled. Median performance error (MDPE), median absolute performance error (MDAPE), and wobble parameters of ScO₂ were calculated before (reference value), during, and… More >

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CASE REPORT

Sara Moufarrij¹, Manisha Gandhi¹, Wilson Lam², Angeline Opina^2,*
Congenital Heart Disease, Vol.16, No.2, pp. 137-139, 2021, DOI:10.32604/CHD.2021.013165
Abstract A 23-year-old female with Tetralogy of Fallot who is 30w6d pregnant presented with palpitations and syncope from an outside hospital. She was found to have ventricular tachycardia. Successful placement of a transvenous implantable cardiac defibrillator allowed for symptomatic control and a subsequent successful vaginal delivery. More >

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ARTICLE

Félix Collard¹, Dimitrios Buklas², Pascale Maragnes¹, Fabien Labombarda^1,*
Congenital Heart Disease, Vol.16, No.2, pp. 141-146, 2021, DOI:10.32604/CHD.2021.013180
Abstract Objective: Abnormal coronary artery origin (ACAO) from the opposite sinus with inter-arterial course of the ectopic proximal vessel is associated with the greatest potential for clinical manifestations, specifically sudden death. Data remain limited regarding the association between bicuspid aortic valve (BAV) and this potentially dangerous coronary variant reported in up to 0.6% in the general population. We investigated the frequency of this high-risk ACAO with inter-arterial course in our surgical series of BAV patients. Methods and Results: We conducted a retrospective study to identify BAV patients with ACAO and inter-arterial course who underwent elective aortic valve/root surgery between 2010 and… More >

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CASE REPORT

Diqi Zhu¹, Xiaohong Gu², Jie Shen^1,*, Fen Li^1,*
Congenital Heart Disease, Vol.16, No.2, pp. 147-150, 2021, DOI:10.32604/CHD.2021.014360
Abstract Background: Communication between the right pulmonary artery (RPA) and left atrium (LA) is a rare cause of central cyanosis in pediatric patients. Case presentation: We describe a 3-year-old female patient with an oxygen saturation of 70% at admission. The echocardiogram indicated an abnormal color flow Doppler in the LA and she underwent standard cardiac catheterization. The angiography of pulmonary artery revealed a 7.4 mm × 7.6 mm fistula between the RPA and LA and achieved successful closure using ventricular septal defect occlusion. Conclusion: The fistula between pulmonary artery and left atrium is an extremely rare but treatable congenital defect. It… More >

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971

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ARTICLE

Hongxiao Sun, Gang Luo, Zhanhui Du, Zhixian Ji, Silin Pan^*
Congenital Heart Disease, Vol.16, No.2, pp. 151-157, 2021, DOI:10.32604/CHD.2021.014770
Abstract Objective: To evaluate the efficacy of Amplatzer duct occluder II (ADO II) in the treatment of perimembranous ventricular septal defect (pmVSD) in children. Methods: Between June 2017 and June 2020, 13 patients with pmVSD had attempted transcatheter closure using ADO II, seven of patients were used antegrade approach and six of them were used retrograde approach. Results: There were 8 males and 5 females, age from 1 to 7 years, weight from 10.5 to 31.0 kg, and VSD size from 2.0 to 4.0 mm. Procedure was successful in all cases with the outer diameter of the occluders ranging from 4… More >

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1131

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ARTICLE

Ruikun Zou¹, Yifei Wang^1,*, Chengcheng Pang², Yunxia Sun¹, Chen Chen¹, Jian Zhuang³
Congenital Heart Disease, Vol.16, No.2, pp. 159-170, 2021, DOI:10.32604/CHD.2021.015050
Abstract Aim: To determine the profiles of clinical features including four-limb blood pressure (BP), saturations of peripheral oxygen (SpO₂), and echocardiographic features in infants with coarctation of aorta (CoA) to facilitate congenital heart diseases screening. Methods: The charts of infants with CoA were retrospectively reviewed. All in-hospital infants suspected of congenital heart diseases by clinical teams were prospectively measured of four limbs BPs and SpO₂ in a regional cardiac transferring center during 2013 and 2019. Echocardiography as a gold standard test was followed within 2 days after suspicion. All infants were divided into non-significant CoA group or significant CoA group based… More >

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ARTICLE

Reghan Conrey^1,*, Sebastian Tume², Carlos Bonilla-Ramirez³, Seema Lalani⁴, Dean McKenzie^3,#, Marc Anders^2,#
Congenital Heart Disease, Vol.16, No.2, pp. 171-181, 2021, DOI:10.32604/CHD.2021.014409
Abstract Background: Patients with genetic syndromes who undergo surgery to correct congenital heart defects can be at risk for increased morbidity or mortality. Surgical outcomes and postoperative courses following congenital heart surgery in patients with Kabuki-Syndrome (KS) have not been well studied. Objectives: The purpose of this study was to describe the postoperative courses and associated outcomes in the largest set of KS patients undergoing congenital heart surgery to date. Methods: Patients with a confirmed molecular diagnosis of KS and a diagnosis of a CHD admitted to Texas Children’s Hospital between January 1, 2000 and January 1, 2020 were included (n… More >

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CASE REPORT

Christopher M. Day^1,*, Neda Mulla², Timothy Martens³, Brent M. Gordon²
Congenital Heart Disease, Vol.16, No.2, pp. 183-187, 2021, DOI:10.32604/CHD.2021.014337
Abstract Marfan syndrome patients have connective tissue abnormalities that predispose them to intracardiac defects and postoperative complications. We present a case of late onset ASD device failure secondary to device movement within the atrial septum in a girl with Marfan syndrome. This case study suggests that further studies are necessary to determine the optimal device and approach for ASD repair in this patient cohort. More >

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REVIEW

Samuel Menahem^1,2,*, Arvind Sehgal^3,4
Congenital Heart Disease, Vol.16, No.2, pp. 189-196, 2021, DOI:10.32604/CHD.2021.014903
Abstract Most congenital heart disease (CHD) is readily recognisable in the newborn. Forewarned by previous fetal scanning, the presence of a murmur, tachypnoea, cyanosis and/or differential pulses and saturations all point to a cardiac abnormality. Yet serious heart disease may be missed on a fetal scan. There may be no murmur or clinical cyanosis, and tachypneoa may be attributed to non-cardiac causes. Tachypnoea on day 1 is usually non-cardiac except arising from ventricular failure or a large systemic arteriovenous fistula. A patent ductus arteriosus (PDA) may support either pulmonary or systemic duct dependent circulations. The initially high pulmonary vascular resistance (PVR)… More >

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