Open Access
ARTICLE
Seul Gi Cha1, Mi Kyung Song1, Sang Yun Lee1, Gi Beom Kim1, Jae Gun Kwak2, Woong Han Kim2, Eun Jung Bae1
Congenital Heart Disease, Vol.14, No.5, pp. 684-690, 2019, DOI:10.1111/chd.12810
Abstract Objective: Cardiovascular lesions are the leading cause of morbidity and mortality in
patients with Williams syndrome. Recent studies have rebutted conventional reports
about the natural course of cardiovascular anomalies in Williams syndrome.
Design: Retrospective study.
Setting: Single tertiary center.
Patients: Eighty patients with Williams syndrome followed up for more than 5 years.
Interventions: Not applicable.
Outcome Measures: Long‐term outcome of cardiovascular lesions, peak velocity
change in obstructive cardiovascular lesions over time, post‐interventional courses
of disease‐specific intervention, and intervention‐free survival of obstructive cardio‐
vascular lesions.
Results: The median follow‐up duration was 11.0 (5.1‐28.3) years. Among 80 pa‐
tients, supravalvular aortic stenosis… More >
Open Access
ARTICLE
Vidhya Annavajjhala1, Rajesh Punn1, Theresa A. Tacy1, Frank L. Hanley2, Doff B. McElhinney2
Congenital Heart Disease, Vol.14, No.5, pp. 691-699, 2019, DOI:10.1111/chd.12772
Abstract Background: Little is known about the early time course of biventricular function and
mechanics after tetralogy of Fallot (TOF) repair. We sought to evaluate and describe
the evolution of the right ventricle (RV) after TOF repair in young infants and children
using conventional echocardiographic parameters and global longitudinal strain
(GLS).
Methods: A retrospective review was performed of all patients with TOF and pulmo‐
nary stenosis who underwent repair from January 2002 to September 2015 and had
at least 3 serial postsurgical echocardiograms spanning from infancy to early child‐
hood (<8 years). Student’s t test was performed to compare patients who… More >
Open Access
ARTICLE
Alexander C. Egbe, Sorin V. Pislaru, Srikanth Kothapalli, Raja Jadav, Muhammad Masood, Mounika Angirekula, Patricia A. Pellikka
Congenital Heart Disease, Vol.14, No.5, pp. 700-705, 2019, DOI:10.1111/chd.12783
Abstract Background: Quantitative assessment of right ventricular (RV) systolic function by
echocardiography is challenging in patients with congenital heart disease because of
the complex geometry of the RV and the iatrogenic structural abnormalities resulting
from prior cardiac surgeries. The purpose of this study was to determine the correla‐
tion between echocardiographic indices of RV systolic function and cardiac magnetic
resonance imaging (CMRI) derived RV ejection fraction (RVEF) in adults with repaired
tetralogy of Fallot (TOF).
Methods: Quantitative assessment of RV function was performed with RV tissue
Doppler systolic velocity (RV s'), tricuspid annular plane systolic excursion (TAPSE),
and fractional area change… More >
Open Access
ARTICLE
Alan F. Riley1, Elena C. Ocampo1, Joseph Hagan2, M. Regina Lantin‐Hermoso1
Congenital Heart Disease, Vol.14, No.5, pp. 706-712, 2019, DOI:10.1111/chd.12774
Abstract Background: When performed by cardiologists, hand‐held echocardiography (HHE)
can assess ventricular systolic function and valve disease in adults, but its accuracy
and utility in congenital heart disease is unknown. In hypoplastic left heart syndrome
(HLHS), the echocardiographic detection of depressed right ventricular (RV) systolic
function and higher grade tricuspid regurgitation (TR) can identify patients who are
at increased risk of morbidity and mortality and who may benefit from additional
imaging or medical therapies.
Methods: Children with HLHS after Stage I or II surgical palliation (Norwood or Glenn
procedures) were prospectively enrolled. Subjects underwent HHE by a pediatric
cardiologist on the… More >
Open Access
ARTICLE
Vidhushei Yogeswaran1, Rahul Kanade1, Camilo Mejia1, Ayotola Fatola1, Srikanth Kothapalli1, Maria Najam1, Harigopal Sandhyavenu1, Mounika Angirekula1, Karim Osma1, Mathews Jessey1, Donald Hagler2, Alexander C. Egbe1
Congenital Heart Disease, Vol.14, No.5, pp. 713-719, 2019, DOI:10.1111/chd.12813
Abstract Background: Although Doppler echocardiography is routinely used to assess left
ventricle cardiac output, there are limited data about the feasibility of Doppler echo‐
cardiography for right ventricular (RV) cardiac output assessment in patients with
left‐to‐right shunt. The purpose of the study was to determine the correlation be‐
tween Doppler‐derived and Fick‐derived RV cardiac index (CI), and the interobserver
correlation in Doppler‐derived RV CI assessment.
Methods: Retrospective study of patients (age ≥18 years) with unrepaired atrial septal
defect who underwent cardiac catheterization and echocardiography (within 3 days),
2004‐2017. RV CI was calculated using the hydraulic orifice formula: [.785 × (right
ventricle… More >
Open Access
ARTICLE
Erin K. Davis1, Salil Ginde1, Jessica Stelter2, Peter Frommelt1, Garick D. Hill3
Congenital Heart Disease, Vol.14, No.5, pp. 720-725, 2019, DOI:10.1111/chd.12814
Abstract Background/Hypothesis/Objectives: Postoperative complications after the Fontan
operation for single ventricle heart disease are common and include persistent pleural drainage and prolonged length of hospital stay (LOS). Diastolic ventricular dysfunction may increase risk for postoperative complications by raising central venous
pressures. We sought to determine the relationship between preoperative echocardiographic measurements of diastolic function, including myocardial deformation
imaging, on (a) preoperative invasive catheterization measurements and (b) postoperative outcomes after the Fontan procedure.
Design/Methods: All patients that underwent Fontan procedure from 2011 to 2017
were included. Echocardiograms performed within 6 months prior to Fontan operation were evaluated. Measurements of ventricular global and… More >
Open Access
ARTICLE
Katherine Awh1,2, Morgan A. Venuti1,2, Lacey P. Gleason1,2, Rachel Rogers3, Srinivas Denduluri1, Yuli Y. Kim1,2
Congenital Heart Disease, Vol.14, No.5, pp. 726-734, 2019, DOI:10.1111/chd.12784
Abstract Objective: To determine the prevalence and predictors of nonattendance in an ACHD
outpatient clinic, and to examine the relationship between nonattendance and emergency department (ED) visits, hospitalizations, and death.
Methods: Patients ≥ 18 years who had scheduled appointments at an ACHD outpatient clinic between August 1, 2014 and December 31, 2014 were included. The
primary outcome of interest was nonattendance of the first scheduled appointment
of the study period, defined as “no-show” or “same-day cancellation.” Secondary outcomes of interest were ED visits, hospitalizations, and death until December 2017.
Results: Of 527 scheduled visits, 55 (10.4%) were nonattended. Demographic and
socioeconomic… More >
Open Access
ARTICLE
Natalie Bottega1, Isabelle Malhamé2, Liming Guo1, Raluca Ionescu‐Ittu1, Judith Therrien1, Ariane Marelli1
Congenital Heart Disease, Vol.14, No.5, pp. 735-744, 2019, DOI:10.1111/chd.12811
Abstract Background: The number of women with congenital heart disease (CHD) of reproductive age is increasing, yet a description of trends in pregnancy and delivery outcomes in this population is lacking.
Objective: To assess secular trends in pregnancy rates, delivery outcomes, and related health care utilization in the adult female CHD population in Quebec, Canada.
Methods: The Quebec CHD database was used to construct a cohort with all women
with CHD aged 18‐45 years between 1992 and 2004. Pregnancy and delivery rates
were determined yearly and compared to the general population. Secular trends in
pregnancy and delivery rates were assessed with… More >
Open Access
ARTICLE
Anudeep K. Dodeja1, Courtney Thomas1, Curt J. Daniels1,2, Naomi Kertesz1,2, Anna Kamp1,2
Congenital Heart Disease, Vol.14, No.5, pp. 745-751, 2019, DOI:10.1111/chd.12815
Abstract Background: Rhythm disorders are the leading cause of morbidity and mortality in
adults with congenital heart disease (ACHD). Infrequent or asymptomatic arrhyth‐
mias may not be detected by routine monitoring. Implantable loop recorders (ILRs),
such as the Reveal LINQTM, have been useful in long‐term monitoring for arrhythmias
in adults with cryptogenic stroke.
Objective: We propose the Reveal LINQTM will detect arrhythmias, not documented
by other monitoring modalities, resulting in change in management in ACHD patients.
Methods: This is a single center retrospective review of Reveal LINQTM use in ACHD
patients from 2014‐2017. Medical records were reviewed to determine cardiac diag‐… More >
Open Access
ARTICLE
Katherine B. Salciccioli1, Abiodun Oluyomi2, Philip J. Lupo3, Peter R. Ermis1, Keila N. Lopez1
Congenital Heart Disease, Vol.14, No.5, pp. 752-759, 2019, DOI:10.1111/chd.12819
Abstract Background: Follow‐up at a regional adult congenital heart disease (ACHD) center
is recommended for all ACHD patients at least once per the 2018 ACC/AHA guidelines. Other specialties have demonstrated poorer follow‐up and outcomes correlating with increased distance from health care providers, but driving time to regional
ACHD centers has not been examined in the US population.
Objective: To identify and characterize potential disparities in access to ACHD care
in the US based on drive time to ACHD centers and compounding sociodemographic
factors.
Methods: Mid‐ to high‐volume ACHD centers with ≥500 outpatient ACHD visits
and ≥20 ACHD surgeries annually were included… More >
Login
Register
Submit a Paper
Propose a Special lssue