Open Access

ARTICLE

Right aortic arch with situs solitus frequently heralds a vascular ring

William N. Evans^1,2, Ruben J. Acherman^1,2, Michael L. Ciccolo^1,3, Sergio A. Carrillo^1,3, Gary A. Mayman^1,2, Carlos F. Luna^1,2, Robert C. Rollins^1,2, William J. Castillo^1,2, Alvaro Galindo^1,2, Abraham Rothman^1,2, John A. Alexander^1,2, Tina W. Kwan^1,2, Humberto Restrepo^1,2

1 Children’s Heart Center Nevada, Las Vegas, Nevada
2 Division of Pediatric Cardiology, Department of Pediatrics, University of Nevada School of Medicine, Las Vegas, Nevada
3 Department of Surgery, University of Nevada School of Medicine, Las Vegas, Nevada

* Corresponding Author: William N. Evans, Children’s Heart Center Nevada, 3006 S. Maryland Parkway Ste. 690, Las Vegas, NV. Email:

Congenital Heart Disease 2017, 12(5), 583-587. https://doi.org/10.1111/chd.12487

Abstract

Objective: We hypothesized that a right aortic arch in situs solitus, with or without an associated cardiovascular malformation, is often associated with a vascular ring.
Methods: From those born in Southern Nevada between March 2012 and March 2017, we identified 50 (3.6 per 10,000 live births) with a right aortic arch and situs solitus. From the 50 patients, 6 did not meet inclusion criteria for further analysis.
Results: Of the 44 remaining, 33 (75%) had a vascular ring. Of the 33 with a vascular ring, 26 (79%) occurred with an isolated right aortic arch, and 7 (21%) had an associated cardiovascular malformation. Of the total 44 patients with a right aortic arch in situs solitus, 34 (79%) were diagnosed prenatally.
Conclusions: In conclusion, we found a right aortic arch in situs solitus was often associated with a vascular ring. Further, to the best of our knowledge, no previous general population study has demonstrated an equal or higher right aortic arch, prenatal detection rate of 79%.

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