Open Access
EDITORIAL
Andrew N. Redington
Congenital Heart Disease, Vol.12, No.5, pp. 559-560, 2017, DOI:10.1111/chd.12527
Abstract This article has no abstract. More >
Open Access
ARTICLE
Elise D. Pieterman1,2, Ricardo P. J. Budde2, Danielle Robbers-Visser1,2, Ron T. van Domburg3, Willem A. Helbing1,2
Congenital Heart Disease, Vol.12, No.5, pp. 561-569, 2017, DOI:10.1111/chd.12484
Abstract Objective: Follow-up of right ventricular performance is important for patients with congenital
heart disease. Cardiac magnetic resonance imaging is optimal for this purpose. However, observerdependency of manual analysis of right ventricular volumes limit its use. Knowledge-based reconstruction is a new semiautomatic analysis tool that uses a database including knowledge of right
ventricular shape in various congenital heart diseases. We evaluated whether knowledge-based
reconstruction is a good alternative for conventional analysis.
Design: To assess the inter- and intra-observer variability and agreement of knowledge-based versus conventional analysis of magnetic resonance right ventricular volumes, analysis was done by
two observers in a mixed… More >
Open Access
ARTICLE
Amir-Reza Hosseinpour1, Mathieu van Steenberghe1, Marc-André Bernath2, Stefano Di Bernardo3, Marie-Hélène Pérez4, David Longchamp4, Mirko Dolci2, Yann Boegli2, Nicole Sekarski3, Javier Orrit1, Michel Hurni1, René Prêtre1, Jacques Cotting4
Congenital Heart Disease, Vol.12, No.5, pp. 570-577, 2017, DOI:10.1111/chd.12485
Abstract Objective: An important aspect of perioperative care in pediatric cardiac surgery is maintenance
of optimal hemodynamic status using vasoactive/inotropic agents. Conventionally, this has
focused on maintenance of cardiac output rather than perfusion pressure. However, this approach
has been abandoned in our center in favor of one focusing primarily on perfusion pressure, which
is presented here and compared to the conventional approach.
Design: A retrospective study.
Setting: Regional center for congenital heart disease. University Hospital of Lausanne,
Switzerland.
Patients: All patients with Aristotle risk score ≥8 that underwent surgery from 1996 to 2012
were included. Patients operated between 1996 and 2005… More >
Open Access
ARTICLE
Trahern W. Jones, Michael D. Seckeler
Congenital Heart Disease, Vol.12, No.5, pp. 578-582, 2017, DOI:10.1111/chd.12486
Abstract Objective: Three-dimensional (3D) printing is a manufacturing method by which an object is created in an additive process, and can be used with medical imaging data to generate accurate
physical reproductions of organs and tissues for a variety of applications. We hypothesized that
using 3D printed models of congenital cardiovascular lesions to supplement an educational lecture
would improve learners’ scores on a board-style examination.
Design and Intervention: Patients with normal and abnormal aortic arches were selected and
anonymized to generate 3D printed models. A cohort of pediatric and combined pediatric/emergency medicine residents were then randomized to intervention and control groups.… More >
Open Access
ARTICLE
William N. Evans1,2, Ruben J. Acherman1,2, Michael L. Ciccolo1,3, Sergio A. Carrillo1,3, Gary A. Mayman1,2, Carlos F. Luna1,2, Robert C. Rollins1,2, William J. Castillo1,2, Alvaro Galindo1,2, Abraham Rothman1,2, John A. Alexander1,2, Tina W. Kwan1,2, Humberto Restrepo1,2
Congenital Heart Disease, Vol.12, No.5, pp. 583-587, 2017, DOI:10.1111/chd.12487
Abstract Objective: We hypothesized that a right aortic arch in situs solitus, with or without an associated
cardiovascular malformation, is often associated with a vascular ring.
Methods: From those born in Southern Nevada between March 2012 and March 2017, we identified 50 (3.6 per 10,000 live births) with a right aortic arch and situs solitus. From the 50 patients,
6 did not meet inclusion criteria for further analysis.
Results: Of the 44 remaining, 33 (75%) had a vascular ring. Of the 33 with a vascular ring, 26
(79%) occurred with an isolated right aortic arch, and 7 (21%) had an associated… More >
Open Access
ARTICLE
Maryanne Caruana1, Victor Grech2
Congenital Heart Disease, Vol.12, No.5, pp. 588-595, 2017, DOI: 10.1111/chd.12488
Abstract Objectives: To investigate survival and freedom from reintervention after aortic coarctation repair
in Maltese patients and to compare cardiovascular mortality in coarctation repair survivors with
that in the general population.
Design: All 72 aortic coarctation patients with any type of repair, born by end-1997 and logged in
the local database were included. Trends in timing and type of repair were determined by comparing patients born before and after 1985. Kaplan-Meier analyses of survival and reintervention-free
survival were performed on the 59 repair survivors with complete follow-up data (mean follow-up
26.13 ± 9.62 (range 1.05–44.55 years). Cardiovascular mortality in repair survivors… More >
Open Access
ARTICLE
Silvana Molossi1,2, Hitesh Agrawal1,2
Congenital Heart Disease, Vol.12, No.5, pp. 596-596, 2017, DOI:10.1111/chd.12490
Abstract Coronary artery anomalies, particularly anomalous aortic origin of a coronary artery with an interarterial course, are associated with sudden cardiac arrest or death in the young. There is paucity of
data on risk stratification and longitudinal follow up is lacking in these patients. Collaboration and
sharing of data among specialized centers might shed much needed light in this complex problem. More >
Open Access
ARTICLE
Mark S. Link
Congenital Heart Disease, Vol.12, No.5, pp. 597-599, 2017, DOI:10.1111/chd.12494
Abstract Sudden cardiac death (SCD), particularly in the young athlete, is a rare though devastating event
for families, institutions, and communities at large. It can also affect the nonathlete and occur at
rest, although most commonly associated with exercise activities and/or sports participation. Common causes of SCD include cardiomyopathies, particularly hypertrophic cardiomyopathy in the
United States, congenital coronary artery anomalies, channelopathies, among others. This report
will explore an overview of the prevalence and causes of SCD in the young. More >
Open Access
ARTICLE
Julie A. Brothers1,2
Congenital Heart Disease, Vol.12, No.5, pp. 600-602, 2017, DOI:10.1111/chd.12497
Abstract Anomalous aortic origin of a coronary artery (AAOCA) occurs when both coronary arteries arise
from the same aortic sinus from a single ostium or two separate ostia. While most coronary
anomalies are benign, the two most common subtypes that predispose to sudden cardiac death in
the young are interarterial anomalous right coronary artery and interarterial anomalous left coronary artery. Practitioners face many challenges with AAOCA. Diagnosing patients may be difficult
because children and adolescents are often asymptomatic and first presentation may be sudden
death or sudden cardiac arrest. Risk stratification is also challenging as determining which unique
characteristics place the… More >
Open Access
ARTICLE
Hitesh Agrawal1,2, Carlos M. Mery1,3, Rajesh Krishnamurthy1, Silvana Molossi1,2
Congenital Heart Disease, Vol.12, No.5, pp. 603-606, 2017, DOI:10.1111/chd.12518
Abstract Anomalous aortic origin of a coronary artery is a congenital abnormality of the origin or course of
a coronary artery that arises from the aorta. As commonly seen in congenital heart disease, a wide
spectrum of anatomic variability is seen and hence, it is important for clinicians to document the
precise anatomy and course of the anomalous vessel. This article describes coronary artery
nomenclature using computerized tomography angiography and virtual angioscopy. These details
are important for decision making, useful for surgical planning, and may have prognostic
implications. More >
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